Conditions once viewed as separate disease entities and now recognised as a manifestation of immunoglobulin G subclass 4-related disease (adapted from Khosroshahi and Stone2)
| Original terminology | Organ target |
| Autoimmune pancreatitis | Pancreas |
| Sclerosing cholangitis | Biliary tree |
| Mikulicz's syndrome | Salivary and lacrimal glands |
| Kuttner's tumour | Submandibular glands |
| Riedel's thyroiditis | Thyroid |
| Retroperitoneal fibrosis (Ormond's disease) | Retro peritoneum |
| Mediastinal fibrosis | Mediastinum |
| Chronic sclerosing aortitis | Aorta |
| Inflammatory abdominal aortitis | Abdominal aorta |
| Orbital pseudotumour | Orbital adnexa |
| Eosinophilic angiocentric fibrosis | Orbits, sinuses and nasal cavities |
| Multifocal fibrosclerosis | Orbits, thyroid gland, retroperitoneum, mediastinum and other tissues |
| Idiopathic hypocomplementaemic tubulointerstitial nephritis with extensive tubulointerstitial deposits | Kidney |