Diagnostic criteria for AIP and IgG4-RD: The Japan–Korea consensus criteria for the diagnosis of AIP10
| I-1 | Pancreatic parenchymal imaging reveals diffuse/segmental/focal gland enlargement, occasionally with a mass and/or a rim of hypo attenuation |
| I-2 | Pancreaticobiliary duct imaging reveals diffuse/segmental/focal duct narrowing, often with stenosis of the bile duct |
| II | Elevated serum IgG or IgG4 concentration and detection of autoantibodies |
| III | Lymphoplasmacytic infiltration of pancreatic tissue with abundant IgG4-positive plasma cells |
A diagnosis of AIP requires the presence of criteria I-1 and I-2 plus either criterion II or criterion III.
AIP, autoimmune pancreatitis; IgG4-RD, immunoglobulin G subclass 4-related disease.