Table 3

Key clinical features of the cases

Case	Demographics (sex, age (years))	Clinical presentation	Relevant history	Radiological characteristics	Serology	Possible other organ manifestations	Surgical treatment	Recurrence
1	Male, 75	AP, weight loss	DM	Focal mass HOP, PD dilated		Pulmonary nodules, retroperitoneal nodes, bulky ampulla	Whipple's	No
2	Male, 74	AP, weight loss	DM	Focal mass HOP, PD dilated		Solitary indeterminate lung nodule, peripancreatic nodes	Total pancreatectomy	No
3	Male, 79	AP		Focal mass HOP and neck, PD dilated, stricture PD			Total pancreatectomy	No
4	Male, 75	AP	DM	Focal mass HOP, PD dilated			Whipple's and postoperative chemotherapy	Yes
5	Male, 66	AP	DM, hypothyroid	Focal mass HOP, pancreatitis, PV thrombus			Whipple's	Yes
6	Male, 67	AP		Focal mass HOP, PD dilated, pancreatitis			Whipple's	No
7	Female, 63	AP, weight loss		Focal mass HOP and uncinate, PD dilated, atrophy			Whipple's	No
8	Female, 57	AP		Focal mass BOP, PD dilated			Whipple's and postoperative chemotherapy	No
9	Male, 72	None		Focal mass HOP, PD dilated			Total pancreatectomy and splenectomy	No
10	Male, 77	Jaundice	Asthma, atopy	Focal mass uncinate, PD dilated, PV thrombosis	sIgG8.87 d/l, sIgG4 0.27 g/l, ANA negative		Whipple's and postoperative chemotherapy	Yes
11	Male, 59	Steatorrhoea		Focal mass HOP, PD dilated			Whipple's	No
12	Male 58	None	Opthalmoplegia (no cause)	Focal mass HOP, PD dilated, atrophy			Total pancreatectomy	No
13	Female, 59	AP		Focal mass TOP, PD dilated			Distal pancreatectomy	Yes
14	Male, 76	None		Focal mass HOP			Whipple's	No

ANA, antinuclear antibody; AP, abdominal pain; BOP, body of pancreas; DM, type 2 diabetes mellitus; HOP, head of pancreas; PD, pancreatic duct; PV portal vein; TOP, tail of pancreas.