Comparative analysis of PEComa classifications
Classification | Benign | UMP | Malignant | ||||
---|---|---|---|---|---|---|---|
Cases, N | Malignant behaviour, N (%) | Cases, N | Malignant behaviour, N (%) | Cases, N | Malignant behaviour, N (%) | Not assessable Cases, N | |
Folpe | 9 | 0 (0) | 5 | 0 (0) | 42 | 29 (69) | 22* |
Modified-Folpe | 29 | 0 (0) | 0 | 0 (0) | 42 | 29 (69) | 7 |
Schoolmeester† | 51 | 7 (14) | 17 | 17 (100) | 10 |
*Fifteen due to Folpe criteria deficits.
†Schoolmeester et al combined the benign and UMP categories.
PEComas, perivascular epithelioid tumours; UMP, uncertain malignant potential.