Table 1

Patient baseline characteristics

Number of patients40
  Gender: male-female50%-50% (20:20)
  Age median (range) (years)55.4 (27–80)
 Age in diagnosis median (range) (years)47.9 (15–77)
Family history
 Positive33.3%
 Positive+sudden death17.9%
Symptoms
 Angina pectoris23%
 Dyspnoea89.7%
 Syncope15.4%
NYHA (I-II-III-IV-NA)20.5-38.5-30.8-2.6-7.7%
History of hypertension46.2%
ECG
 LVH signs76.9%
 T wave inversion89.7%
 Normal ECG17.9%
 QTc interval (ms) median (range)450, 1 (360–552)
Echo
 IVS thickness (mm) median (range)19.1 (8–30)
 PW thickness (mm) median (range)11.6 (3–20)
 LV end-diastolic diameter (mm) median (range)45.5 (28–64)
 LV end-systolic diameter (mm) median (range)25.8 (12–47)
 LA end-systolic diameter (mm) median (range)45.5 (31–67)
NMR28/11
 Systolic blood pressure (mm Hg) median (range)127.6 (100–179)
 Diastolic blood pressure (mm Hg) median (range)77.5 (60–95)
  • IVS, interventricular septum; LA, left atrium; LV, left ventricle; LVH, left ventricular hypertrophy; NMR, nuclear magnetic resonance; NYHA, New York Heart Association Functional Classification; PW, posterior wall.