Patient baseline characteristics
Number of patients | 40 |
Gender: male-female | 50%-50% (20:20) |
Age median (range) (years) | 55.4 (27–80) |
Age in diagnosis median (range) (years) | 47.9 (15–77) |
Family history | |
Positive | 33.3% |
Positive+sudden death | 17.9% |
Symptoms | |
Angina pectoris | 23% |
Dyspnoea | 89.7% |
Syncope | 15.4% |
NYHA (I-II-III-IV-NA) | 20.5-38.5-30.8-2.6-7.7% |
History of hypertension | 46.2% |
ECG | |
LVH signs | 76.9% |
T wave inversion | 89.7% |
Normal ECG | 17.9% |
QTc interval (ms) median (range) | 450, 1 (360–552) |
Echo | |
IVS thickness (mm) median (range) | 19.1 (8–30) |
PW thickness (mm) median (range) | 11.6 (3–20) |
LV end-diastolic diameter (mm) median (range) | 45.5 (28–64) |
LV end-systolic diameter (mm) median (range) | 25.8 (12–47) |
LA end-systolic diameter (mm) median (range) | 45.5 (31–67) |
NMR | 28/11 |
Systolic blood pressure (mm Hg) median (range) | 127.6 (100–179) |
Diastolic blood pressure (mm Hg) median (range) | 77.5 (60–95) |
IVS, interventricular septum; LA, left atrium; LV, left ventricle; LVH, left ventricular hypertrophy; NMR, nuclear magnetic resonance; NYHA, New York Heart Association Functional Classification; PW, posterior wall.